Proposed Three-Tier Staging of Rhinoorbitocerebral Mucormycosis.7
| Stage | Details |
|---|---|
| Stage 1: Sinonasal Involvement | 1A: Involvement of 1 sinus and ipsilateral middle turbinate |
| 1B: Involvement of >1 ipsilateral sinus and/or turbinate | |
| 1C: Involvement of bilateral sinonasal cavities | |
| Stage 2: Orbital Involvement | 2A: Involvement of medial and/or inferior orbital compartment only |
| 2B: Diffuse unilateral orbital involvement with or without optic nerve, nasolacrimal duct, and vascular involvement | |
| 2C: Bilateral orbital involvement | |
| Stage 3: Central Nervous System Involvement | 3A: Involvement of pachymeninges, cribriform plate, cavernous sinus/Meckel’s cave |
| 3B: Vascular involvement (infarct/bleed)/perineural spread and skull base involvement | |
| 3C: Leptomeningitis, cerebritis or abscess formation—focal or diffuse involvement |