Table 1.

Proposed Three-Tier Staging of Rhinoorbitocerebral Mucormycosis.7

Stage Details
Stage 1: Sinonasal Involvement 1A: Involvement of 1 sinus and ipsilateral middle turbinate
1B: Involvement of >1 ipsilateral sinus and/or turbinate
1C: Involvement of bilateral sinonasal cavities
Stage 2: Orbital Involvement 2A: Involvement of medial and/or inferior orbital compartment only
2B: Diffuse unilateral orbital involvement with or without optic nerve, nasolacrimal duct, and vascular involvement
2C: Bilateral orbital involvement
Stage 3: Central Nervous System Involvement 3A: Involvement of pachymeninges, cribriform plate, cavernous sinus/Meckel’s cave
3B: Vascular involvement (infarct/bleed)/perineural spread and skull base involvement
3C: Leptomeningitis, cerebritis or abscess formation—focal or diffuse involvement
RMMJ Rambam Maimonides Medical Journal Rambam Health Care Campus 2022; 13(4): e0024. ISSN: 2076-9172
Published online 2022 October 27. doi: 10.5041/RMMJ.10483