Table 2.

Differences Between Fasting and Non-fasting Hereditary Coproporphyria (HCP) and Variegate Porphyria (VP) Patients.

Parameter Fasting Patients (n=30) Non-fasting Patients (n=31) P Value
Age (mean±SD) 50.7±17.5 43.6±17.1 0.7
Female (n, %) 15 (44.1%) 15 (48%) 0.89
Smokers (n, %) 10 (33%) 15 (48%) 0.23
Alcohol use >1 drink/week (n, %) 1 (3.3%) 3 (9.7%) 0.32
HCP patients, n=21 (n, %) 13 (57.5%) 8 (25.8%) 0.15
VP patients, n=40 (n, %) 17 (42.5%) 23 (74.2%)
Previously had acute porphyria symptoms (n, %) 17 (56.6%) 26 (83.8%) 0.19
Previously visited ED due to porphyria (n, %) 10 (33%) 13 (41.9%) 0.48
Previously received heme treatment (n, %) 2 (6.6%) 3 (9.7%) 0.66
ED visits for porphyria symptoms within 1 week after fast (n visits/patient years) 1/383 (0.26%) 1/383 (0.26%) 1.0
ED visits for porphyria symptoms within 1 month after fast (n visits/patient years) 3/383 (0.78%) 8/383 (2.1%) 0.12

ED, emergency department.

RMMJ Rambam Maimonides Medical Journal Rambam Health Care Campus 2023 January; 14(1): e0003. ISSN: 2076-9172
Published online 2023 January 29. doi: 10.5041/RMMJ.10490